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Centre de référence pour les maladies rares

Hereditary Rhythmic Diseases and Prevention of Sudden Death

Reference Center for Hereditary Rhythmic diseases and for the prevention of Sudden death (in charge: Prof. Frederic Sacher)


Our reference center takes charge of patients with inherited arrhythmic diseases i.e. (Brugada Syndrome, Long QT syndrome, Arrhythmogenic right ventricular dysplasia…) and patients with a high risk of sudden death.  The patient care is located at the Hospital Haut-Lévêque, Service of Prof. Haïssaguerre - Cardiology Unit.


For many years, our team has been working on scientific methods for a better understanding of the causes of ventricular fibrillation (main cause of sudden death), to develop innovative therapeutic treatments (percutaneous cauterization on areas provoking these arrhythmias) and to ensure a better health care for patients: In 2003, we developed a new technology, the telecardiology, and we participated to numerous studies within a national registry.


The creation of the Liryc institute (Electrophysiology and heart modeling Institute) in 2011, has allowed us to explore new fields of research around these pathologies.


In the early years of 2000, we were able to organize & homogenize the full care of these patients in the Aquitaine region.  We have also put into place a family screening of patients with hereditary rhythmic diseases thanks to the collaboration of Dr Caroline Thambo (genetic dept.) and the establishment of joint consultations  (cardiologist and geneticist).


Following the « state-of-the art » intervention skills developed here to better treat ventricular-fibrillation, we now treat patients from all over metropolitan France, from overseas and from Europe for the treatment of the most complex cases.


We are also involved in risk prevention, through ongoing education of practitioners and cardiologists through EPU, training courses, worldly convention meetings, but mostly through a specific web site developed by Prof. Bordachar in order to allow practitioners to familiarize themselves with useful aspects of the ECG signals allowing them to identify these pathologies.  (


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